Left ventricular-Right atrial canal is a rare congenital heart disease. The vast majority of the cases reported in the literature are clinically diagnosed as atrial septal defect or ventricular septal defect. The method of choice in establishing the diagnosis of left ventricular-right atrlal canal is selective left ventriculography. Recently we experienced one case of left ventricular-right atrial canal which was diagnosed as ventricular septal defect preoperatively. The type of defect was tricuspid perforation of infravalvular type, and repaired with direct suture. Postoperative course was uneventful and discharged without complication.