This is a case report of extralobar pulmonary sequestration with bronchogenic cyst located in aorto-pulmonary window area of left thorax in a 17 months old male patient. In this case, a bronchogenic cyst was presented immediately adjacent to the extralobar pulmonary sequestration. Communication between the extralobar pulmonary sequestration and bronchogenic cyst was not seen grossly or microscopically. The lesion was simply excised and the postoperatively course was uneventful.