Pulmonary leiomyosarcoma는 대부분 전이된 예로서, 원발성으로 나타나는 경우는 극히 드물다. 저자들은 우폐하엽부에 발생한 종괴를 경피침흡인법과 우폐하엽 절제술을 통한 조직검사로 진단하고 전이여부에 대한 추후검사를 시행한 결과 원발성 폐평활근육종으로 확진된 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.
Primary Pulmonary leiomyosarcomas are rare tumors. These tumors may arise at any level of the lung in which smooth muscle fibers are found. The highest incidence of sarcoma is during the fourth decade whereas for bronchogenic carcinoma the maximum incidence is during the sixth and seventh decades. Leiomyosarcomas are aggressive and progressive. Treatment is mainly surgical. The chemotherapy is ineffective and the effectiveness of radiotherapy depends on the total dose of irradiation. Prognosis and significant survival rate are related to the size of the lesion. We report one patient with primary pulmonary leiomyosarcoma involving the right lower lung.
