A choristoma is a tumor like mass of normal tissue in an abnormal location. Lingual osseous choristoma, previously known as osteoma of the tongue base, is rare entity. That is defined as a normal bone mass occuring in the soft tissue of either the skin or the mucosa of oral cavity. The cause of osseous choristoma of the tongue is still unknown, but only several theories have been suggested. Because of the rarity of this entity, our purpose is to add our case to the literature, and to discuss the nature of the disease.