Granular cell tumor is an uncommon lesion that was first described by Abrikossoff in 1926. It is usually benign tumor that can occur in any parts of the body. The most common region of granular cell tumor is the head and neck, accounting for approximately 30 to 50 percent of all lesions, with the tongue as the single most common site of origin. The larynx is uncommon location, accounting for approximately 3 to 10 percent of the reported case. Herein we report a case of a 41-year-old man with laryngeal granular cell tumor who was successfully treated, especially showing well improvements in his voice after the operation. In addition, a brief discussion of the current literatures regarding the typical features of the tumor are also presented.