Complete interruption of the aortic arch is one of the least common cardiac malformation. In this condition, continuity between the ascending and descending protions of the aorta is not present, and the descending aorta is supplied through a reversing patent ductus arteriosus. In the majority of the patients a ventricular septal defect is present. Authors have expierenced a case of the complete interruption of aortic arch, interruption between the left carotid and the left subclavian artery.